[Term] id: PR:000041193 name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform 1 def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q6P3A8-1 or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=sequence. synonym: "BCKDHB/iso:1" EXACT PRO-short-label [PRO:DNx] property_value: has_archetype PR:Q6P3A8-1 is_a: PR:000004687 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial