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Protein Ontology report - 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human)
PR:P21953 - http://purl.obolibrary.org/obo/PR_P21953
 
  Protein Forms      
Ontology Information Show OBO stanza / GPI
  PRO ID
PR:P21953   
  PRO name2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) 
  Synonyms
PRO-Short-label: EXACT:hBCKDHB
Gene-based: RELATED:BCKDHB
Other: EXACT:BCKDE1B (human) | BCKDH E1-beta (human) | branched-chain alpha-keto acid dehydrogenase E1 component beta chain (human)
  Definition"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:P21953] 
  PRO Categoryorganism-gene 
  ParentPR:000004687 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
PR:000029067 Homo sapiens protein
  Gene TemplateHGNC:987 BCKDHB (human)
  TaxonNCBITaxon:9606 Homo sapiens
  Terms by PRO Category
Organism-Independent Organism-Specific
         Category          Number of Terms          Category          Number of Terms
         Gene0                                                  Organism-Gene 1                                        
         Sequence0                                                  Organism-Sequence 2                                        
         Modification0                                                  Organism-Modification 10                                        
  Term Hierarchy
  Visualization
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Related Cross References

  Db identifiers
UniProtKB:P21953
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Protein Forms Switch to Compact View   

Category  
PRO ID
Name
Short Name
Definition
Ann. Has Annotation?

Comp. In Complex?
organism-gene


PR:P21953
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human)
hBCKDHB
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:P21953]

organism-sequence


PR:P21953-1
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform h1 (human)
hBCKDHB/iso:h1
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:P21953-1." [PRO:DNx, UniProtKB:P21953]

organism-sequence


PR:P21953-2
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform h2 (human)
hBCKDHB/iso:h2
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:P21953-2." [PRO:DNx, UniProtKB:P21953]

organism-modification


PR:000046472
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial, transit peptide removed form (human)
hBCKDHB/TransPep-
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that has had the transit peptide removed. UniProtKB:P21953, 51-392." [PRO:DNx, Reactome:R-HSA-70015]

organism-modification


PR:000062476
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial, transit peptide removed phosphorylated 1 (human)
hBCKDHB/TransPep-/Phos:1
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that has had the transit peptide removed and that has been phosphorylated on the residue at the position equivalent to Ser-342 of the amino acid sequence represented by UniProtKB:P21953-1. Example: UniProtKB:P21953-1, 51-392, Ser-342, MOD:00046." [PRO:DNx, Reactome:R-HSA-5693124]

organism-modification


PR:000085816
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial sequence variant G278S, transit peptide removed form (human)
hBCKDHB/var:G278S/TransPep-
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that has a Ser residue at the position equivalent to Gly-278 of the amino acid sequence represented by UniProtKB:P21953-1 and that has had the transit peptide removed. Example: UniProtKB:P21953-1, 51-392, Gly-278, CHEBI:29999." [PRO:DNx, Reactome:R-HSA-9865069]

organism-modification


PR:000085865
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial sequence variant Q346R, transit peptide removed form (human)
hBCKDHB/var:Q346R/TransPep-
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that has an Arg residue at the position equivalent to Gln-346 of the amino acid sequence represented by UniProtKB:P21953-1 and that has had the transit peptide removed. Example: UniProtKB:P21953-1, 51-392, Gln-346, CHEBI:29952." [PRO:DNx, Reactome:R-HSA-9865060]

organism-modification


PR:000085904
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial sequence variant N176Y, transit peptide removed form (human)
hBCKDHB/var:N176Y/TransPep-
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that has a Tyr residue at the position equivalent to Asn-176 of the amino acid sequence represented by UniProtKB:P21953-1 and that has had the transit peptide removed. Example: UniProtKB:P21953-1, 51-392, Asn-176, CHEBI:46858." [PRO:DNx, Reactome:R-HSA-9865063]

organism-modification


PR:000085906
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial sequence variant R170H, transit peptide removed form (human)
hBCKDHB/var:R170H/TransPep-
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that has a His residue at the position equivalent to Arg-170 of the amino acid sequence represented by UniProtKB:P21953-1 and that has had the transit peptide removed. Example: UniProtKB:P21953-1, 51-392, Arg-170, CHEBI:29979." [PRO:DNx, Reactome:R-HSA-9865071]

organism-modification


PR:000085988
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial sequence variant R183P, transit peptide removed form (human)
hBCKDHB/var:R183P/TransPep-
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that has a Pro residue at the position equivalent to Arg-183 of the amino acid sequence represented by UniProtKB:P21953-1 and that has had the transit peptide removed. Example: UniProtKB:P21953-1, 51-392, Arg-183, CHEBI:50342." [PRO:DNx, Reactome:R-HSA-9865041]

organism-modification


PR:000086004
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial sequence variant H206R, transit peptide removed form (human)
hBCKDHB/var:H206R/TransPep-
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that has an Arg residue at the position equivalent to His-206 of the amino acid sequence represented by UniProtKB:P21953-1 and that has had the transit peptide removed. Example: UniProtKB:P21953-1, 51-392, His-206, CHEBI:29952." [PRO:DNx, Reactome:R-HSA-9865047]

organism-modification


PR:000071288
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial methylated 1 (human)
hBCKDHB/Me:1
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that has been methylated on the residue at the position equivalent to Cys-207 of the amino acid sequence represented by UniProtKB:P21953-1. Example: UniProtKB:P21953-1, Cys-207, MOD:00660." [IEDB_epitope:999551, PRO:DNx]

organism-modification


PR:000079222
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial methylated 2 (human)
hBCKDHB/Me:2
"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that has been methylated on the residue at the position equivalent to Cys-299 of the amino acid sequence represented by UniProtKB:P21953-1. Example: UniProtKB:P21953-1, Cys-299, MOD:00660." [IEDB_epitope:1029378, PRO:DNx]